Published date: Jun 30 2022

Journal Title: Sudan Journal of Medical Sciences

Issue title: Sudan JMS: Volume 17 (2022), Issue No. 2

Pages: 252–262

DOI: 10.18502/sjms.v17i2.11459

Shokouh Taghipour ZahirFull Professor of Clinical and Surgical Pathology, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

Mehran MortazNeurosurgeon, Mortaz Hospital, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

Koorosh RahmaniGeneral Practitioner, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

Farzan Safi Dahajsafi.farzan@gmail.comIran

Desmoplastic infantile astrocytoma/ganglioglioma (DIA/DIG) is a rare mixed neuronalglial solid cystic brain tumor found in infantile cerebral hemispheres. The main presentation of the tumor is the rapidly enlarging of the head circumference with hydrocephalus and seizure. DIA is classified as a WHO Grade 1 brain tumor but, due to the rarity of the tumor, few studies are available on tumor survival and prognosis. Herein, we report a 47-day-old male infant diagnosed with DIA and the four-year follow-up.

Keywords: brain neoplasm, astrocytoma, pediatric neurosurgery, oncology, desmoplastic cerebral astrocytoma of infancy, desmoplastic infantile ganglioglioma

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