Journal of Ophthalmic and Vision Research

ISSN: 2008-322X

The latest research in clinical ophthalmology and the science of vision.

Glaucoma in Ectropion Uveae Syndrome: a Case Report and Literature Review

Published date: Jul 18 2019

Journal Title: Journal of Ophthalmic and Vision Research

Issue title: July–September 2019, Volume 14, Issue 3

Pages: 370–375

DOI: 10.18502/jovr.v14i3.4793

Authors:

Mohammadmehdi Hatami - drmehdihatami@gmail.com - https://orcid.org/0000-0003-2733-7802

Azadeh Doozandeh

Mohadeseh Feizi

Abstract:

Purpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU).

Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP.

Conclusion: Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.

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