Published date: Apr 19 2023

Journal Title: Journal of Ophthalmic and Vision Research

Issue title: April–June 2023, Volume 18, Issue 2

Pages: 212–229

DOI: 10.18502/jovr.v18i2.13188

Richard BrownDepartment of Ophthalmology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, USA

Sashwanthi MohanRajan Eye Care Hospital, Chennai, India

Jay Chhablanijay.chhablani@gmail.comDepartment of Ophthalmology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, USA

Pachychoroid disease spectrum is a recent term that has been associated with an increasing number of phenotypes. This review discusses updated findings for each of the typical pachychoroid entities (central serous chorioretinopathy, pachychoroid pigment epitheliopathy, pachychoroid neovasculopathy, polypoidal choroidal vasculopathy, peripapillary pachychoroid syndrome, and focal choroidal excavation), as well as two relatively new additions (peripapillary pachychoroid neovasculopathy and peripheral exudative hemorrhagic chorioretinopathy). Here, we discuss the potential pathogenic mechanisms for these diseases and relevant imaging updates. Finally, we argue for a consistent classification scheme for these entities.

Keywords: Central Serous Chorioretinopathy, Choroid, Pachychoroid, Focal Choroidal Excavation, Pachychoroid Neovasculopathy, Peripapillary Pachychoroid Syndrome, Peripapillary Pachychoroid Neovasculopathy, Polypoidal Choroidal Vasculopathy, Retinopathy

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